The medications-to-avoid line

Every note built here carries the list — aminoglycosides, fluoroquinolones, macrolides, intravenous magnesium, beta-blockers, botulinum toxin, quinine derivatives, checkpoint inhibitors, neuromuscular blockers, and high-dose steroids without cover — because the most common preventable trigger of crisis is a well-meant prescription written by someone who did not know the diagnosis.

Extubation is a plan, not an event

When you mark the patient intubated, the builder writes the extubation criteria (NIF and FVC thresholds, cough, secretion burden, immunotherapy under way for two to three days), the pyridostigmine hold and restart, and the avoidance of neuromuscular blockers. Electrolytes matter here too: hypokalemia and hypophosphatemia worsen weakness and get their own line.

Beyond the crisis

The note closes with the steroid-sparing agent, thymoma imaging if not yet done, the neuromuscular clinic follow-up, and the crisis action plan and medication card the patient leaves with.

Frequently asked questions

What is the 20/30/40 rule?

A bedside mnemonic for impending respiratory failure in neuromuscular disease: forced vital capacity under 20 mL/kg, negative inspiratory force weaker than −30 cmH2O, or maximal expiratory pressure under 40 cmH2O. The builder writes the thresholds and, above all, that the trend matters more than any single value.

IVIG or plasma exchange?

Overall efficacy is similar. The builder writes plasma exchange as faster and preferred in MuSK-positive disease or when IVIG is contraindicated (IgA deficiency, renal failure, hypercoagulable states), and IVIG when the patient is hemodynamically unstable or has poor vascular access.

Why does the plan hold pyridostigmine while intubated?

It reduces secretions and removes the confusion between myasthenic and cholinergic weakness during the acute phase; the builder writes a low-dose restart before extubation.

References

  1. Sanders DB, et al. International consensus guidance for management of myasthenia gravis: 2020 update. Neurology. 2021;96:114–122.
  2. Gajdos P, et al. Clinical trial of plasma exchange and high-dose intravenous immunoglobulin in myasthenia gravis. Ann Neurol. 1997;41:789–796.
  3. Wolfe GI, et al. Randomized trial of thymectomy in myasthenia gravis (MGTX). N Engl J Med. 2016;375:511–522.
  4. Wendell LC, Levine JM. Myasthenic crisis. Neurohospitalist. 2011;1:16–22.